Neža Salobir
Zdravstveni dom Ljubljana, Ljubljana, Slovenija

Janez Jazbec
Klinični oddelek za otroško hematologijo in onkologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana, Ljubljana, Slovenija in Katedra za pediatrijo, Medicinska fakulteta, Univerza v Ljubljani, Ljubljana, Slovenija

Jože Maučec
Klinični oddelek za otroško kirurgijo, Kirurška klinika, Univerzitetni klinični center Ljubljana, Ljubljana, Slovenija

Abstract

Neuroendocrine tumours of the appendix (aNET) are slow-growing, indolent tumours that have an excellent prognosis and rarely show regional nodal metastases. They account for 0.1% of malignant tumours in children. The treatment and follow-up of aNET in children is not standardised. Appendectomy alone is considered curative in most patients, while a more aggressive surgical approach is warranted for incompletely removed tumours or tumours larger than 2 cm. In the last 11.5 years, 23 children and adolescents were diagnosed with aNET in Slovenia.

Key words: appendix, neuroendocrine tumour, carcinoid, child