Mateja Starbek Zorko
Otroški oddelek, Dermatovenerološka klinika, Univerzitetni klinični center Ljubljana, LJubljana, Slovenija in Katedra za dermatovenerologijo Medicinska fakulteta, Univerza v Ljubljani

Abstract

Pityriasis lichenoides et varioliformis acuta (PLEVA), also known as Mucha-Habermann disease, is an uncommon cutaneous inflammatory disease that mostly affects children and young adults. It usually presents as an acute eruption of inflammatory macules, papules or papulovesicles, which quickly develop haemorrhagic or necrotic crusts. The most severe presentation of the disease is febrile ulceronecrotic Mucha-Habermann disease (FUMHD), which can be potentially life-threatening. This is the reason why we should recognise and start the right treatment of the disease in time.

Key words: Pityriasis lichenoides, PLEVA, Mucha-Habermann, children, young adults